Percentage of subjects with juvenile macular dystrophy or retinitis pigmentosa responding to activities at each level of difficulty
| Activity | χ2 | df | p Value | Level of difficulty | Did not perform for non-visual reasons | Group | |||||||
|---|---|---|---|---|---|---|---|---|---|---|---|---|---|
| None | Mild | Moderate | Extreme | Not able | |||||||||
| Activities involving central vision: | |||||||||||||
| Threading a needle | 32.8 | 4 | 0.001 | 2.8 | 12.5 | 1.4 | 13.9 | 45.8 | 23.6 | JMD | |||
| 20.0 | 15.0 | 13.3 | 5.0 | 18.3 | 28.3 | RP | |||||||
| Reading street signs at night | 57.7 | 4 | 0.001 | 0.0 | 9.7 | 15.3 | 12.5 | 62.5 | 0.0 | JMD | |||
| 14.2 | 25.0 | 27.5 | 20.0 | 11.7 | 1.7 | RP | |||||||
| Reading directions on medicine bottles | 59.9 | 4 | 0.001 | 8.3 | 12.5 | 15.3 | 19.4 | 44.4 | 0.0 | JMD | |||
| 39.2 | 28.3 | 13.3 | 11.7 | 4.2 | 3.3 | RP | |||||||
| Reading ingredients on cans of food | 88.4 | 4 | 0.001 | 6.9 | 8.3 | 15.3 | 19.4 | 45.8 | 4.2 | JMD | |||
| 51.7 | 25.0 | 12.5 | 4.2 | 2.5 | 4.2 | RP | |||||||
| Reading street signs during the day | 79.1 | 4 | 0.001 | 2.8 | 11.1 | 26.4 | 20.8 | 38.9 | 0.0 | JMD | |||
| 39.2 | 33.3 | 19.2 | 5.8 | 2.5 | 0.0 | RP | |||||||
| Seeing faces across a street | 67.6 | 4 | 0.001 | 2.8 | 11.1 | 5.6 | 0.0 | 79.2 | 1.4 | JMD | |||
| 40.0 | 25.8 | 10.0 | 2.5 | 20.8 | 0.8 | RP | |||||||
| Reading ordinary newspaper print | 84.9 | 4 | 0.001 | 5.6 | 19.4 | 15.3 | 8.3 | 50.0 | 1.4 | JMD | |||
| 55.0 | 29.2 | 10.0 | 1.7 | 3.3 | 0.8 | RP | |||||||
| Playing cards | 49.0 | 4 | 0.001 | 19.4 | 33.3 | 12.5 | 5.6 | 16.7 | 12.5 | JMD | |||
| 59.2 | 11.7 | 5.0 | 5.8 | 0.0 | 18.3 | RP | |||||||
| Reading numbers on TV screen | 56.8 | 4 | 0.001 | 19.4 | 29.2 | 20.8 | 5.6 | 23.6 | 1.4 | JMD | |||
| 70.8 | 20.0 | 5.8 | 0.8 | 2.5 | 0.0 | RP | |||||||
| Finding destination/unfamiliar buildings | 21.8 | 3 | 0.001 | 15.3 | 37.5 | 29.2 | 16.7 | 0.0 | 1.4 | JMD | |||
| 46.7 | 31.7 | 14.2 | 7.5 | 0.0 | 0.0 | RP | |||||||
| Mobility: | |||||||||||||
| Finding a seat in a movie theatre | 35.5 | 3 | 0.001 | 45.8 | 18.1 | 8.3 | 13.9 | 0.0 | 13.9 | JMD | |||
| 11.7 | 12.5 | 28.3 | 30.0 | 0.0 | 17.5 | RP | |||||||
| Finding particular items in a store | 8.7 | 3 | 0.034 | 31.9 | 29.2 | 18.1 | 5.6 | 0.0 | 15.3 | JMD | |||
| 51.7 | 25.0 | 7.5 | 5.0 | 0.0 | 10.8 | RP | |||||||
| Walking outdoors at night | 35.9 | 4 | 0.001 | 52.8 | 18.1 | 11.1 | 2.8 | 13.9 | 1.4 | JMD | |||
| 14.2 | 24.2 | 25.8 | 15.0 | 18.3 | 2.5 | RP | |||||||
| Participating in social gatherings | 4.0 | 4 | 0.408 | 51.4 | 29.2 | 13.9 | 0.0 | 2.8 | 2.8 | JMD | |||
| 41.7 | 33.3 | 19.2 | 2.5 | 1.7 | 1.7 | RP | |||||||
| Walking through shopping malls | 27.9 | 4 | 0.001 | 70.8 | 13.9 | 11.1 | 2.8 | 1.4 | 0.0 | JMD | |||
| 31.7 | 29.2 | 22.5 | 9.2 | 6.7 | 0.8 | RP | |||||||
| Negotiating steps: | |||||||||||||
| Walking down steps in dim light | 42.6 | 4 | 0.001 | 45.8 | 29.2 | 2.8 | 0.0 | 20.8 | 1.4 | JMD | |||
| 11.7 | 17.5 | 22.5 | 6.7 | 34.2 | 7.5 | RP | |||||||
| Walking down steps during daylight | 18.4 | 4 | 0.001 | 62.5 | 22.2 | 2.8 | 0.0 | 11.1 | 1.4 | JMD | |||
| 34.2 | 24.2 | 12.5 | 5.8 | 18.3 | 5.0 | RP | |||||||
| Driving: | |||||||||||||
| Driving at night | 5.3 | 4 | 0.259 | 5.6 | 9.7 | 5.6 | 1.4 | 13.9 | 63.9 | JMD | |||
| 11.7 | 18.3 | 16.7 | 13.3 | 16.7 | 23.3 | RP | |||||||
| Driving during the day | 15.0 | 4 | 0.005 | 5.6 | 23.6 | 2.8 | 2.8 | 1.4 | 63.9 | JMD | |||
| 37.5 | 29.2 | 10.0 | 1.7 | 0.0 | 21.7 | RP | |||||||
| Driving in unfamiliar areas | 10.2 | 4 | 0.038 | 0.0 | 11.1 | 11.1 | 2.8 | 8.3 | 66.7 | JMD | |||
| 15.0 | 30.8 | 12.5 | 6.7 | 8.3 | 26.7 | RP | |||||||
| Eating: | |||||||||||||
| Eating meals | 1.8 | 2 | 0.420 | 88.9 | 9.7 | 1.4 | 0.0 | 0.0 | 0.0 | JMD | |||
| 86.7 | 8.3 | 5.0 | 0.0 | 0.0 | 0.0 | RP | |||||||
| Miscellaneous: | |||||||||||||
| Writing checks | 36.4 | 4 | 0.001 | 40.3 | 16.7 | 5.6 | 6.9 | 12.5 | 18.1 | JMD | |||
| 83.3 | 5.0 | 1.7 | 0.8 | 1.7 | 7.5 | RP | |||||||
| Engaging in physical exercise | 2.8 | 4 | 0.587 | 65.3 | 19.4 | 4.2 | 0.0 | 4.2 | 6.9 | JMD | |||
| 62.5 | 23.3 | 7.5 | 0.8 | 1.7 | 4.2 | RP | |||||||
| Watching a movie at a theatre | 3.1 | 4 | 0.537 | 47.2 | 22.2 | 11.1 | 5.6 | 8.3 | 5.6 | JMD | |||
| 48.3 | 16.7 | 14.2 | 1.7 | 6.7 | 12.5 | RP | |||||||
| Using a ruler | 46.0 | 4 | 0.001 | 23.6 | 27.8 | 23.6 | 8.3 | 9.7 | 6.9 | JMD | |||
| 70.0 | 14.2 | 5.8 | 2.5 | 0.8 | 6.7 | RP | |||||||
| Walking outdoors during the day | 2.3 | 4 | 0.682 | 68.1 | 20.8 | 8.3 | 1.4 | 1.4 | 0.0 | JMD | |||
| 73.3 | 16.7 | 8.3 | 0.0 | 1.7 | 0.0 | RP | |||||||
| Preparing meals | 8.7 | 2 | 0.013 | 59.7 | 29.2 | 8.3 | 0.0 | 0.0 | 2.8 | JMD | |||
| 78.3 | 14.2 | 4.2 | 0.0 | 0.0 | 3.3 | RP | |||||||
| Grooming | 5.4 | 3 | 0.144 | 76.4 | 20.8 | 2.8 | 0.0 | 0.0 | 0.0 | JMD | |||
| 85.0 | 10.0 | 3.3 | 1.7 | 0.0 | 0.0 | RP | |||||||
| Using a screwdriver | 23.3 | 4 | 0.001 | 47.2 | 26.4 | 15.3 | 1.4 | 1.4 | 8.3 | JMD | |||
| 70.0 | 11.7 | 1.7 | 5.0 | 0.8 | 10.8 | RP | |||||||
| Using escalators | 6.2 | 3 | 0.104 | 86.1 | 8.3 | 1.4 | 0.0 | 4.2 | 0.0 | JMD | |||
| 70.0 | 19.2 | 4.2 | 0.0 | 5.0 | 1.7 | RP | |||||||
| Watching television | 40.0 | 4 | 0.001 | 36.1 | 31.9 | 20.8 | 9.7 | 1.4 | 0.0 | JMD | |||
| 80.0 | 12.5 | 6.7 | 0.8 | 0.0 | 0.0 | RP | |||||||
| Grocery shopping | 15.3 | 4 | 0.004 | 27.8 | 36.1 | 13.9 | 5.6 | 6.9 | 9.7 | JMD | |||
| 56.7 | 20.8 | 9.2 | 1.7 | 6.7 | 5.0 | RP | |||||||
| Using public transport | 11.9 | 4 | 0.018 | 25.0 | 26.4 | 15.3 | 8.3 | 2.8 | 22.2 | JMD | |||
| 40.8 | 15.0 | 9.2 | 1.7 | 1.7 | 31.7 | RP | |||||||









