Editor,—Sebaceous carcinoma (SC) of the eyelid and palpebral conjunctiva is rare.1 We present a patient with this entity and Muir-Torre syndrome (MTS).2 3 MTS is characterised by the concurrent or sequential documentation of at least a single sebaceous gland tumour (adenoma, epithelioma, or carcinoma), with or without keratoacanthomas, and a minimum of one internal malignancy. A recent review revealed that 163 cases fulfilling the diagnostic criteria for MTS have been reported since 1913, with 318 internal malignancies.4-6 Colorectal (47%) and urogenital (21%) malignancies predominate, and nearly half the patients have two or more internal cancers. Our case is remarkable and was previously reported 7 years ago for presenting the highest number of malignancies described in this syndrome (eleven) and a prolonged survival of 26 years.7