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  • Bilaminar interepithelial bodies within fingerprint dystrophy-like changes in bilateral iridocorneal endothelial syndrome

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Bilaminar interepithelial bodies within fingerprint dystrophy-like changes in bilateral iridocorneal endothelial syndrome
  1. C Auw-Haedrich1,
  2. U Sengler2,
  3. W R Lee3
  1. 1Universitäts-Augenklinik Freiburg, Germany
  2. 2Universitäts-Augenklinik Düsseldorf, Germany
  3. 3Department of Pathology, University of Glasgow, Scotland, UK
  1. Correspondence to: Dr Claudia Auw-Haedrich, Universitäts-Augenklinik, Killianstrasse 5, D-79106 Freiburg, Germany; auw{at}aug.ukl.uni-freiburg.de

https://doi.org/10.1136/bjo.87.4.508-a

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    In most cases the iridocorneal endothelial (ICE) syndrome affects women unilaterally and shows endothelial degeneration, thickening of Descemet's membrane, iris atrophy, and glaucoma. The spectrum of the ICE syndrome includes the Chandler's syndrome, the essential iris atrophy, and the Cogan-Reese syndrome. We present a unique case of an ICE syndrome, which we would subclassify as Chandler's syndrome, with concomitant fingerprint dystrophy and multiple interepithelial bilaminar bodies within the fingerprint-like striae.

    Case Report

    Ten years earlier a now 45 year old patient presented with a bilateral ICE syndrome and fingerprint dystrophy. On slit lamp microscopy the epithelial layer showed fingerprint lines, while the endothelial layer had a “hammered” appearance. Iris atrophy, corectopia, ectropium uveae and anterior synechiae were obvious (Fig 1A) and progressive in both eyes, nevertheless the intraocular pressure and the visual acuity were normal. Eight years later both corneas developed oedema (Fig 1B) and the left eye displayed cataract with reduction of visual acuity from 1.0 to …

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