Echographic features of a case of malignant intraocular medulloepithelioma

Intraocular medulloepithelioma is a rare embryonal neoplasm, usually presenting in the first decade of life as a unilateral, cystic ciliary body mass arising from the non-pigmented ciliary epithelium. Histologically, medulloepithelioma is classified as non-teratoid (a pure proliferation of medullary epithelial cells) or teratoid (containing heteroplastic elements such as hyaline cartilage, skeletal muscle or neuroglial tissue).^1,2 Either group can be subclassified as benign or malignant, the latter showing evidence of poor differentiation, increased mitotic activity, and local invasion with or without extraocular extension.²

We report the progressive echographic findings in a case of malignant intraocular medulloepithelioma. Echographic examination, by B-scan (10 MHz probe) and high resolution anterior segment scan (20 MHz probe), was performed during two examinations under anaesthesia (EUA), using the I3 system.

Case report

An 18 month old girl presented with a distorted pupil apparently following a fall downstairs some 4 weeks previously. Her …