Electrophysiological abnormalities in patients with AZOOR
| Electrophysiological measure | Normal range (min–5%; max+5% | Median | Range | 25th centile | 75th centile |
|---|---|---|---|---|---|
| ERG, electroretinogram; PERG, pattern ERG; EOG, electro-oculography. | |||||
| Pattern ERG (μV) | >2.0 | 1.2 | 0.0–3.2 | 0.0 | 2.2 |
| EOG light rise (Arden index) | 130 | 100–300 | 100 | 200 | |
| Interocular EOG light rise difference (10 unilateral cases only) | 80 | 40–200 | 45 | 125 | |
| Scotopic rod ERG amplitude (μV) | 152–452 | 105 | 0–275 | 45 | 150 |
| Scotopic rod ERG latency (ms) | 78–108 | 89 | 48–133 | 85 | 105 |
| Maximal ERG a-wave amplitude (μV) | 261–495 | 165 | 0–405 | 86 | 255 |
| Maximal ERG a-wave latency (ms) | 9–15 | 12 | 10–13 | 11 | 13 |
| Maximal ERG b-wave amplitude (μV) | 366–866 | 270 | 0–555 | 120 | 400 |
| 30 Hz flicker amplitude (μV) | 68–226 | 40 | 0–155 | 15 | 65 |
| 30 Hz flicker latency (ms) | 23–28 | 30 | 24–46 | 27 | 36 |
| Photopic ERG b-wave implicit time | 26–34 | 32 | 26–42 | 30 | 36 |
| Photopic ERG b-wave amplitude | 101–336 | 70 | 0–190 | 25 | 103 |
| ON-b-wave amplitude (μV) | 31 | 0–52 | 16 | 43 | |
| ON-b-wave latency (ms) | 35 | 33–46 | 34 | 36 | |
| OFF-d-wave amplitude (μV) | 49 | 0–93 | 10 | 67 | |
| OFF-d-wave latency (ms) | 223 | 221–230 | 223 | 225 | |









