Retinal changes in juvenile X linked retinoschisis using three dimensional optical coherence tomography
- Department of Ophthalmology, Asahikawa Medical College, Asahikawa, Japan
- Correspondence to: Satoshi Ishiko Department of Ophthalmology, Asahikawa Medical College, 2-1 Midorigaoka Higashi, Asahikawa, 078-8316, Japan; ishikoasahikawa-med.ac.jp
- Accepted 29 July 2005
Juvenile X linked retinoschisis is a congenital X linked recessive retinal disorder, the characteristic funduscopic findings of which are a silver-grey retinal reflex, foveal retinoschisis, and peripheral retinoschisis. Electroretinograms (ERGs) typically record a reduced b-wave amplitude with relative preservation of the a-wave amplitude. Visual acuity (VA) usually deteriorates slowly until the patient is about 20 years of age, stabilises around 0.2~0.5, and sometimes deteriorates further because of macular degeneration.1–4
Podoleanu and associates developed a novel integration of scanning laser ophthalmoscopy (SLO) and optic coherence tomography (OCT)—three dimensional optical coherence tomography (3-D OCT).5 Using transverse scanning, typical for SLO, the instrument simultaneously produces SLO and interferometric OCT images.6 We can obtain both cross sectional scans (B-scans) as with conventional OCT and transverse scans (C-scans) using 3-D OCT. This is the first report of 3-D OCT findings in juvenile X linked retinoschisis.
Case report
A 7 year old boy presented with VA of 0.5 …
