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Vitreoretinal surgery without schisis cavity excision for the management of juvenile X linked retinoschisis
  1. J García-Arumí1,
  2. I A Corcóstegui1,
  3. R Navarro1,
  4. M A Zapata2,
  5. M H Berrocal3
  1. 1
    Instituto de Microcirugía Ocular (IMO), Barcelona, Spain
  2. 2
    Hospital Valle de Hebrón, Universidad Autónoma de Barcelona, C/ Aureli Campmany, Sant Cugat del Valles, Barcelona, Spain
  3. 3
    University of Puerto Rico School of Medicine, Río Piedras, Puerto Rico
  1. Dr M A Zapata, Hospital Valle de Hebrón, Universidad Autónoma de Barcelona, C/ Aureli Campmany 2–10, Esc 3 1°, 2a 08195, Sant Cugat del Valles Barcelona, Spain; zapatavictori{at}hotmail.com

Abstract

Juvenile X linked retinoschisis (XLRS) is a congenital X linked recessive retinal disorder characterised by cystic maculopathy and peripheral schisis. This study presents the case of an 8-month-old boy with a documented positive family history of XLRS, with a large retinoschisis cavity affecting the macula, first in the left eye and 1 year later in the right eye. The patient underwent pars plana vitrectomy in both eyes using 23-G instruments, posterior hyaloid dissection, a small retinotomy, fluid drainage with a 42-G cannula, infrared diode laser and silicone oil as internal tamponade. The anatomical and functional outcomes at 3 years following the first surgery are described. To the authors’ knowledge, there is no previously reported experience with this technique in patients with XLRS.

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Footnotes

  • Competing interests: None.

  • Ethics approval: Ethics approval was provided by Comité ético del Instituto de microcirugia (IMO), Barcelona, Spain.

  • Patient consent: Parental consent was obtained.

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