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X linked retinoschisis (XLRS) is a frequent cause of macular dystrophy in males with an estimated prevalence of between 1 in 15 000 and 1 in 30 000. The diagnosis is based on the presence of central and peripheral schisis within the inner retina and supported by electroretinography, which shows a characteristic electronegative response to a bright flash in the dark-adapted state.1
Fundus related perimetry or microperimetry is a useful tool for assessing macular function and mapping central visual fields, scotomas and fixation behaviour.2 The MP-1 microperimeter (Nidek technologies, Padua, Italy) utilises an LCD microperimeter and allows a direct correlation of macular function with pathology.
We present an observational study of nine patients (17 eyes) aged between 7.5 years and 20 years (median age 10 years) with XLRS who underwent …