Article Text

other Versions

PDF
High-definition spectral domain optical coherence tomography in the evaluation of ataxia with visual impairment
  1. Neeraj Kumar*,
  2. Jose Pulido
  1. Mayo Clinic, United States
  1. Correspondence to: Neeraj Kumar, Mayo Clinic, 200 First St Sw, Rochester, 55905, United States; kumar.neeraj{at}mayo.edu

Abstract

A 36-year old man was evaluated for a 10 year history of visual decline and 5 year history of gait, limb, and speech ataxia. His neurologic exam was remarkable for a wide based ataxic gait with appendicular, axial, and speech ataxia. His eye exam revealed saccadic pursuits and reduced visual acuity. Ophthalmoscopic evaluation of the fundus was remarkable for diffuse attenuation of the arterioles and minimal foveal fine pigmentary mottling. A full-field electroretinogram revealed abnormalities that tended to be more prominent in cone mediated responses. Visual field assessment showed increased blind spot and a left pericentral scotoma. Fluorescein angiography showed a small central window defect in the macula (Figure A). High-definition spectral domain optical coherence tomography (SD-OCT) showed the reason for the reduced visual acuity (Figure B).

Statistics from Altmetric.com

Footnotes

    Request permissions

    If you wish to reuse any or all of this article please use the link below which will take you to the Copyright Clearance Center’s RightsLink service. You will be able to get a quick price and instant permission to reuse the content in many different ways.