Aim: To describe the fluorescein angiographic, fundus autofluorescence, and optical coherence tomography (OCT) findings in patients with a unique unilateral lesion of the temporal macula previously named torpedo maculopathy.
Method: This study was a retrospective, observational case series. The medical records of thirteen patients, age 1 to 68 years, seen between 1982 to 2009 were reviewed. Patients were evaluated for lesion features and course on follow-up, visual acuity, fluorescein angiography, visual field defects, fundus autofluorescence, and OCT findings.
Results: In all thirteen patients, the lesion was flat, torpedo shaped, solitary and involved the temporal macula. The hypopigmented lesion had well-defined margins and a characteristic leading edge which pointed toward the center of the macula. Fluorescein angiography revealed transmission hyperfluorescence of the lesion. OCT indicated a thin abnormal retinal pigment epithelium (RPE) signal and Humphrey Visual Field (HVF) testing revealed a corresponding blind spot. Fundus autofluorescence performed on one patient was dark in the affected area.
Conclusion: Torpedo maculopathy is an apparently congenital hypopigmented torpedo-shaped lesion of the temporal macula. Although it may result in a corresponding visual field defect, these non-foveal lesions do not affect central visual acuity.