Table 4

Comparison of ophthalmic features in type 1 Stickler syndrome and Wagner syndrome

Stickler syndromes Wagner syndrome
MyopiaCongenital, high degreeUsually mild
Anterior chamber angle dysgenesisOccasionalUnreported
CataractWedge-shaped, corticalEarly onset, nuclear, progressive, “cataracta  complicata”
Frequently non-progressive
Type 1 vitreous anomalyPresentAbsent
RetinopathyFrequently normalProgressive pigmentory and punched out  chorioretinal atrophy
 scalloped paravascular pigmented lattice
Retinal detachmentCommon, frequently bilateralUncommon
High risk of giant retinal tear
Dark adaptationNormalMay be reduced