Table 2

Electrophysiological data of patients with Sorsby fundus dystrophy

Patient		Age (years)		Visual acuity		Dark adaptation (threshold log unit)		EOG (Arden index)		ERG response
Patient		Age (years)		RE	LE	Dark adaptation (threshold log unit)		RE	LE	photopic	scotopic
II,5	60	1.0	1.0	1.5 log U ↑	118%	111%	slight↓	severe↓
II,8	74	0.01	0.05	2 log U ↑	100%	100%	slight↓	absent
III,9	46 60	1.0 1.0	1.0 1.0	normal 1 log U ↑	np 120%	np 111%	normal slight↓	normal severe↓
III,10	49 56 59	1.0 1.0 0.8	1.0 1.0 0.8	np 1 log U ↑ 1 log U ↑	118% 120% np	120% 111% np	normal slight↓ severe↓	normal severe↓ absent
III,15	49	0.01	1.0	2 log U ↑	123%	128%	slight↓	severe↓