Age/sex | Duration of disease (years) | Ocular complications | Steroids (local/systemic) |
85/F | 18 | None | –/– |
63/M | 13 | None | –/+ |
62/F | 40 | Keratoconjunctivitis sicca | –/+ |
70/F | 20 | Keratoconjunctivitis sicca | –/– |
71/F | 18 | Keratoconjunctivitis sicca | –/– |
75/F | 20 | Bilateral corneal melt; bilateral ECCE + PKP | +/+ |
77/F | 20 | Left corneal melt; right central thinning; left PKP | +/– |
63/M | Unknown | Left peripheral thinning |
ECCE = extracapsular cataract extraction; PKP = penetrating keratoplasty.