Table 1

Ocular features described in incontinentia pigmenti

Part of the eye affected	Description
Lids	Ptosis²¹
Nasolacrimal duct	Congenital obstruction²⁸
Control of eye movements	Strabismus^1,^7,^17,^19,^21,²³
	Nystagmus^22,²³
Abnormalities of globe size	Microphthalmos²³
	Buphthalmos²²
Conjunctiva	Hyperpigmentation²⁹
Sclera	Blue^19,²⁰
Corneal abnormalities	See text
Iris	Atrophy with pigmentary irregularities²³
	Hypoplasia and synaechiae⁷
Lens	Congenital cataract (usually associated with retinal detachment)^1,^7,^22,²³
Vitreous	Persistent fetal vasculature³⁰
	Haemorrhage
Fovea	Foveal hypoplasia³¹
	Macular aneurysms^8,⁹
Peripheral retina	Fibrovascular proliferation and traction retinal detachment^15,^17,^22,^25,³¹
	Vascular anomalies—eg, microaneurysms, arteriovenous shunts, neovascularisation associated with an avascular zone^8,^9,^17,^23,³²
Optic disc	Neovascularisation³³
	Atrophy^1,^7,^17,³²
RPE	Pigmentary changes^13,^15,^23,^29,³⁴