Table 1

Clinical features of patients

Case NoAge at diagnosisISG criteriaAdditional featuresLength of disease to diagnosisTreatment requiredHLA-B51 status
145YAneurysm 2Prednisolone/azathioprineNeg
226NNeurological 3Anti-TB/prednisoloneND
331YThrombosis 0Prednisolone/azathioprine/tacrolimus/mycophenolate/cyclosporinNeg
420Y 2Prednisolone/cyclosporin/mycophenolateNeg
535YIntestinal and neurological disease 0Prednisolone/azathioprineNeg
630Y 1Prednisolone/azathioprineNeg
734YArthralgia10Azathioprine/prednisolone/colchicineNeg
832Y 3Topical prednisoloneND