Table 1
Serum ANCA specificity in untreated disease
PR3-ANCA
MPO-ANCA
Negative
Adapted from Jennette
et al.
4
Microscopic polyangiitis
40%
50%
10%
Wegener’s granulomatosis
75%
20%
5%
Churg-Strauss syndrome
10%
60%
30%