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Bilateral macular staphylomas in a patient with cone dystrophy
  1. R S Apte1,2,
  2. J S Sunness1,
  3. B G Goldstein2,
  4. W L Park3,
  5. J S Sunness3,
  6. R Z Raden4,
  7. M J Elman4
  1. 1The Retinal Vascular Center, The Wilmer Ophthalmological Institute, The Johns Hopkins University School of Medicine, Baltimore, MD, USA
  2. 2The Vitreoretinal Division
  3. 3Lions Vision Center
  4. 4Elman Retina Group, PA, Baltimore, MD, USA
  1. Correspondence to: Janet S Sunness, MD, The Wilmer Ophthalmological Institute, The Johns Hopkins University School of Medicine, 550 N Broadway, 6th Floor, Baltimore, MD 21205, USA; jsunness{at}jhmi.edu

https://doi.org/10.1136/bjo.87.8.1049-a

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    A posterior staphyloma is characterised by scleral ectasia and is pathognomonic for pathological myopia.1,2 Posterior staphylomas are classified in to five types based on the anatomic location.1 Type 1 staphylomas extend from the nasal border of the optic nerve into the macular region and are the most frequent staphyloma seen in myopes.1 Type 2 staphylomas are centred on the macula while type 3 staphylomas are centred on the optic disc without macular extension.1 Type 4 staphylomas are located nasal to the optic disc and type 5 staphylomas develop inferior to the optic disc.1 Staphylomas can be associated with multiple complications including retinal pigment epithelial atrophy, lacquer cracks, retinal and subretinal haemorrhages, and choroidal neovascularisation.1,3

    This report describes a patient with undiagnosed, bilateral type 2 macular staphylomas compounded by cone dystrophy. To the best of our knowledge, this is a novel association not reported in the literature and with potential therapeutic implications.

    Case report

    A 32 year old white woman presented to the Wilmer Ophthalmological Institute, Baltimore, MD, for a second opinion. She …

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    Footnotes

    • Financial interests: None.

    • Financial support: None.