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Ciliary body medulloepithelioma associated with pleuropulmonary blastoma
  1. Philip W Laird,
  2. Hans E Grossniklaus,
  3. G Baker Hubbard
  1. Department of Ophthalmology, Emory Eye Center, Emory University, Atlanta, Georgia, USA
  1. Correspondence to Dr Philip W Laird, Department of Ophthalmology, Emory Eye Center, Emory University, 1365 Clifton Road, Atlanta, GA 30322, USA; plaird{at}emory.edu

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Case

A 7-year-old African-American girl was found to have reduced vision in the right eye on routine screening. Visual acuity was hand motions in the right eye and 20/20 in the left eye. Intraocular pressure was 17 mm Hg in each eye. Slit-lamp examination of the right eye showed a normal anterior segment, but immediately posterior to the lens was an opaque vascularised cyclitic membrane that blocked the visualisation of the vitreous and retina (figure 1A). The blood vessels appeared to originate superiorly. Fluorescein angiography was performed, which showed brisk circulation and late staining of the cyclitic membrane (figure 1B,C). B-scan ultrasound showed an elevated cystic ciliary body lesion at 12:30 o'clock with irregular internal reflectivity, no apparent calcification and a height of 2.4 mm and basal diameters of 8.4 and 6.6 mm (figure 1D).

Figure 1

(A) The right eye contains a vascularised cyclitic membrane obscuring view into vitreous cavity. (B) Fluorescein angiography 43 s after injection of dye highlights the rich vasculature of the cyclitic membrane. (C) Fluorescein angiography 1 min 35 s after injection of dye shows late staining of the cyclitic membrane. (D) B-scan ultrasonography revealed an elevated cystic ciliary body tumour at 12:30 with a height of 2.4 mm and basal diameters of 8.4 and 6.6 mm. (E) CT …

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Footnotes

  • Contributors GBH conceptualised the idea to create this article. He also reviewed and provided critical editing to the manuscript text. He acquired and interpreted data used in this article. HEG reviewed and provided critical editing to the manuscript text. He acquired and interpreted data used in this article. PWL performed the literature search, drafted the manuscript, acquired and interpreted data and takes responsibility for the overall content as guarantor. All authors contributed to the acquisition and interpretation of data, drafting and revising the article, and final approval. PWL is the guarantor of this article.

  • Funding This research was supported in part by an unrestricted grant from Research to Prevent Blindness, Inc, New York; and by Core Grant EYO 6360 from the National Institutes of Health, Bethesda, Maryland, USA.

  • Patient consent Obtained.

  • Competing interests None.

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