Patients with ophthalmoplegia of undetermined cause
Patient No | Age (years ) | Sex | Pattern of palsy | Anti-GQlb IgG antibody titre | Steroid treatment | Period for recovery | Neurological signs | Neuroimaging study |
---|---|---|---|---|---|---|---|---|
1 | 24 | F | R, VI | <10 | + | 4 m | R, proptosis | CT, MRI |
2 | 64 | M | L, VI | <10 | + | 3 m | — | CT |
3 | 56 | M | L, VI | <10 | − | 2 w | — | — |
4 | 52 | F | B, total | <10 | + | 1 y | — | CT, MRI |
5 | 47 | M | R, So | <10 | + | 3 m | — | — |
6 | 73 | F | B, VI | <10 | − | 2 m | ataxic gait | CT |
7 | 40 | M | B, VI | <10 | + | 3 w | — | CT, MRI |
8 | 62 | F | R, total | 20 | + | 3 m | — | CT |
9 | 51 | M | R, VI | <10 | + | 4 m | — | CT, MRI |
10 | 45 | M | R, total | <10 | + | 4 m | R, proptosis | CT |
11 | 57 | M | L, VI | <10 | + | 6 m | decreased reflex | CT |
12 | 69 | M | L, So | <10 | − | 4 m | — | CT |
13 | 56 | F | B, VI | 640 | + | 2 m | areflexia | CT |
14 | 37 | M | GPN | <10 | − | 1 m | — | CT, MRI |
15 | 40 | F | L, So | <10 | + | 4 m | — | MRI |
16 | 61 | M | R, total+L, VI | <10 | — | 4 m | — | CT |
B = bilateral; VI = abducens palsy; total = total ophthalmoplegia; Sr = superior rectus muscle palsy; So = superior oblique muscle palsy; GPN = gaze paretic nystagmus; m = month(s), w = week(s), y = year(s); CT = head CT scan; MRI = magnetic resonance imaging.