Table 1 Ocular and extraocular involvement in juvenile localised scleroderma
Patient no.GenderSubtypeOcular involvementOcular findingsExtraocular findings
1FECDSAAEyelid abnormalities
2MECDSAAEyelash abnormalities
3MGMAAEyelid abnormalitiesArthritis
4MECDSAAEyelid–eyelash abnormalitiesAortic insufficiency
5FECDSAAEyelid abnormalitiesArthritis
6MECDSAAEctropion
7FECDSAAEyelid abnormalities
8FLinearAAEyelid abnormalities
9MGMAADry eye
10FECDSAAEyelid abnormalities
11FECDSASIAnterior uveitis
12FPMASIAnterior uveitis
13FECDSASIAnterior uveitis
14MLinearASIAnterior uveitis, glaucomaRaynaud phenomenon
15FLinearASIAnterior uveitis
16MLinearASIEpiscleritisPeripheral neuropathy
17FECDSASIEpiscleritisCNS abnormalities
18FECDSCNS-RAPupillary mydriasisEpilepsy
19FECDSCNS-RAPupillary mydriasis, left orbital myositisPseudotumour cerebri
20FECDSCNS-RAEnophalmos, iris subatrophy, stellar neuroretinitis, retinal teleangieactasiaeCNS abnormalities
21FECDSMParalytic strabismus
22FLinearMPseudopapilloedema
23FECDSMRefractive errorEpilepsy
24MECDSMRefractive errorAbnormal pulmonary function tests
  • AA, adnexa abnormalities; ASI, anterior segment inflammation; CNS, central nervous system; CNS-RA, central nervous system-related abnormalities; ECDS, en coup de sabre; GM, generalised morphea; M, miscellanea; PM, plaque morphea.