Table 2

Ocular and electrophysiology findings

Patient no.VA at presentation (age, months)Most recent VA (age, months)DVMNystagmusStrabismusRefractive errorFundusCVIERGFlash VEPPattern-reversal VEPPattern onset VEPStep VEP acuity
1Momentary eye contact (3)6/19, 6/19 (20)XTNormalNormalNormalRaised
26/12 BEO (14)6/19, 6/15 (28)NormalNormalRaised
36/76 BEO (13)NormalNormal
46/48 BEO (6)6/9.5 BEO (11)NormalNormalRaised
56/38 BEO (7)6/24 * BEO (25)NormalNormalDelayed and smallAbnormalAbnormal
66/130 BEO (7)6/9.5 BEO (20)NormalNormalNormalNormal
76/19, 6/12 (63)ETNormalNormalNormal
86/18 * 6/15 * (48)NormalNormalNormalRaised
96/76 BEO (6)5/6, 5/6 (51)HANormalNormalNormalAbsentRaised
106/30 by VEP (7)NKNormalDelayedNormalRaised
116/24 BEO (13)6/24 BEO (18)NormalSmallNormal
126/500 BEO (3)6/120, 6/9.5 (35)XTMA (right eye only)Vessels across maculaNormalDelayedRaised
13Not F&F (2)6/6, 6/6 (68)Possible MTNormalNormal
146/500 BEO (3)6/9.5, 6/15 (46)XTHNormalRaised
15F&F (5)6/12 * 6/12 * (60)NormalNormalNormal
166/120 BEO (8)3/18, 3/18, 3/12 BEO (45)HANormalNormalNormalRaised
17f but not f (3)6/12 BEO (22)NormalNormalAbsentNormal
186/19, 6/15 * (71)NormalNormal
196/24 BEO (27)6/36 BEO (37)ETHASlight disc pallorNormalNormal
206/60, 6/13 (77)ANormalNormalDelayedRaised
  • A, astigmatism; BEO, both eyes open; CVI, cerebral visual impairment; DVM, delayed visual maturation; ERG, electroretinogram; ET, esotropia; F&F, fixing and following; H, hypermetropia; M, myopia; MT, microtropia; VA, visual acuity; XT, exotropia; VEP, visual evoked potential.

  • * Visual acuity (VA) in Snellen equivalent. For visual acuity, the age at testing (in months) is given in brackets next to test findings.