Table 2

Keratoplasty outcomes

MPS IHMPS IH/SMPS ISMPS IVMPS VI
BCVA at last follow-up
 Visual acuity success63722
 No change or unknown13104
 Deterioration10002
Graft clarity
 Success86825
 Rejection episodes04 in 1 eye6 in 2 eyes04 in 4 eyes
 Graft failure00003
Associated ophthalmic findings
 Glaucoma/ocular hypertension24315
 Optic neuropathy12013
 Retinal degeneration02200
  • BCVA, best-corrected visual acuity; MPS, mucopolysaccharidoses; MPS IH, Hurler syndrome; MPS IH/S, Hurler-Scheie syndrome; MPS IS, Scheie syndrome; MPS IV, Morquio syndrome; MPS VI, Maroteaux-Lamy syndrome.