MPS IH | MPS IH/S | MPS IS | MPS IV | MPS VI | |
---|---|---|---|---|---|
BCVA at last follow-up | |||||
Visual acuity success | 6 | 3 | 7 | 2 | 2 |
No change or unknown | 1 | 3 | 1 | 0 | 4 |
Deterioration | 1 | 0 | 0 | 0 | 2 |
Graft clarity | |||||
Success | 8 | 6 | 8 | 2 | 5 |
Rejection episodes | 0 | 4 in 1 eye | 6 in 2 eyes | 0 | 4 in 4 eyes |
Graft failure | 0 | 0 | 0 | 0 | 3 |
Associated ophthalmic findings | |||||
Glaucoma/ocular hypertension | 2 | 4 | 3 | 1 | 5 |
Optic neuropathy | 1 | 2 | 0 | 1 | 3 |
Retinal degeneration | 0 | 2 | 2 | 0 | 0 |
BCVA, best-corrected visual acuity; MPS, mucopolysaccharidoses; MPS IH, Hurler syndrome; MPS IH/S, Hurler-Scheie syndrome; MPS IS, Scheie syndrome; MPS IV, Morquio syndrome; MPS VI, Maroteaux-Lamy syndrome.