Table 1

Group 1, orbital IgG4-RD with or without systemic involvement (cases 1–20 had serology)

NoSiteSexRaceAgeHistologyTissue involvedSystemic IgG4-RDTiss IgGTiss IgG2Tiss IgG4IgG2:IgG (%)IgG4:IgG (%)IgG2:IgG4sIg G1sIg G2sIg G3sIg G4
1SGFCh61Chronic OIDOrbitalNo2006914534730.486.876.981.532.45
2SGFCh76Chronic OIDOrbitalNo1666110037600.617.738.581.472.69
3SGMCh70Chr inflammationLacrimalNo211121206570.19.8416.11.2812.5
4SGFMa30Chronic OIDOrbitalNo133308023600.388.494.472.131.47
5UKMCau33Chr inflammationLacrimalNo2788015429550.525.342.880.461.06
6UKFCau57Chr inf with XGLacrimalNo1057707670.16.367.240.260.38
7UKFCau62Chr inflammationLacrimalNo3364921715650.236.728.571.335.75
8SGMCh55Sclerosing infOrbitalNo1613612222760.304.484.390.952.69
9SGFCh67Chr inflammationLacrimalNo24310813444550.817.737.261.471.66
10SGMCh41Chronic OID with XGOrbitalAutoimmune pancreatitis2979320331680.467.656.10.81.78
11SGMCh61Chr inflammationLacrimalAutoimmune pancreatitis2796221322760.296.365.410.342.76
12SGMCh57Chr inflammationLacrimalMikulicz3225126816830.197.165.120.483.4
13SGMCh58Chr inflammationLacrimalMikulicz32511820036620.596.9717.82.030.76
14SGMCh68Chronic OIDOrbitalMikulicz26610615339570.696.35200.790.52
15SGMM62Chr inflammationLacrimalRenal IgG438181947500.956.6415.870.980.41
16SGFCh52Chr inflammationLacrimalMikulicz2706519024700.348.56201.420.29
17SGMCh67Chr inflammationLacrimalRadiology evidence163249815600.2410.219.961.830.76
18SGMCh68Chr inflammationLacrimalMikulicz100265026500.5210.5610.681.040.72
19UKMCh65Chr inflammationLacrimalMikulicz2062512412600.211.6614.313.020.71
20UKMInd62Chr inflammationLacrimalOther organ IgG42909919134660.5210.114.52.190.23
21SGFCh61Chr inflammationLacrimalNo155509832640.51NANANANA
22SGFOth50Sclerosing infOrbitalNo24210113242550.77NANANANA
23SGFCh77Chr inflammationLacrimalNo7295013690.18NANANANA
24SGFCh66Sclerosing infLacrimalNo2809818035640.54NANANANA
25SGFCh82Chr inflammationOrbitalNo76126016790.2NANANANA
26SGMMa79Chr inflammationLacrimalNo24110912645520.87NANANANA
27SGMCh62Chr inflammationOrbitalNo24311512647520.91NANANANA
28SGFMa48Chr inflammationLacrimalNo98346035610.57NANANANA
29SGFMa37Chr inflammationLacrimalNo16010806500.13NANANANA
30UKMInd67Sclerosing infLacrimalNo3736925518680.27NANANANA
31UKFAfr21Sclerosing infTarsusNo181819445520.86NANANANA
32UKMCh43Chr inflammationLacrimalNo24511612747520.91NANANANA
33UKMInd56Sclerosing infOrbitalNo2595320920800.25NANANANA
34UKMCau68Chr inf with XGOrbitalNo1471911313770.17NANANANA
35UKMCau35Chr inflammationLacrimalNo29011114638500.76NANANANA
36UKFInd40Chr inflammationLacrimalNo3564928314790.17NANANANA
37UKMInd56Chr inflammationLacrimalNo167161419.5840.11NANANANA
38UKMInd44Sclerosing infOrbitalNo2258812939570.68NANANANA
39UKFInd60Sclerosing infLacrimalNo2933324011820.14NANANANA
40SGMCh74Chronic inflammationLacrimalMikulicz2055710228500.56NANANANA
41SGMMa46Sclerosing infLacrimalRadiology evidence2052713913680.19NANANANA
42SGMCh64Sclerosing InfLacrimalRadiology evidence2043511217550.31NANANANA
43UKFCau47Chr infLacrimalOther organ IgG41863014816780.2NANANANA
  • Afr, African; Cau, Caucasian white; Ch, Chinese; Chr, chronic; F, female; Ind, Indian; IgG4-RD, IgG4-related disease; inf, inflammation; Ma, Malay; M, male; NA, Not applicable; OID, orbital inflammatory disorders; Oth, others; SG, Singapore; sIg, serum Ig; Tiss, tissue; UK, United Kingdom; XG, xanthogranulomatous.