Disease/Patient number | Sex | Age | Measured eye | VA logMAR | Full-field ERGs scotopic/photopic | Eccentric fixation | % MP1 fixation 2° | % MP1 fixation 4° | MP fixation stability | Number of pRF mapping runs | pRF stability (MAE) (°) | Framewise displacement (mm) |
STGD 1 | F | 20 | OD | 0.1 | n/n | No | 99 | 100 | Stable | 3 | 0.91 | 0.17±0.03 |
STGD 2 | F | 35 | OD | 0.9 | n/n | Yes | 62 | 95 | Relatively unstable | 3 | 2.56 | 0.35±0.03 |
STGD 3 | F | 50 | OD | 0 | n/n | No | 100 | 100 | Stable | 4 | 0.75 | 0.13±0.01 |
STGD 4 | F | 73 | OD | 0.9 | n/n | Yes | 11 | 42 | Unstable | 2 | 0.51 | 0.64±0.23 |
STGD 5 | F | 33 | OD | 0.9 | n/n | Yes | 20 | 70 | Unstable | 4 | 1.62 | 0.18±0.01 |
STGD 6 | F | 18 | OS | 0.5 | n/n | No | 93 | 99 | Stable | 4 | 0.96 | 0.16±0.01 |
STGD 7 | F | 27 | OS | 0.7 | n/n | No | 67 | 98 | Relatively unstable | 4 | 0.62 | 0.17±0.02 |
STGD 8 | M | 21 | OD | 0.9 | n/n | Yes | 45 | 84 | Relatively unstable | 4 | 0.96 | 0.26±0.03 |
RP 1 | M | 46 | OD | 0.1 | u/u | No | 99 | 100 | Stable | 4 | 0.62 | 0.28±0.05 |
RP 2 | F | 47 | OD | 0 | u/u | No | 98 | 100 | Stable | 4 | 0.67 | 0.22±0.03 |
RP 3 | M | 51 | OS | 0.1 | u/u | No | 95 | 99 | Stable | 2 | / | 0.27±0.04 |
RP 4 | F | 42 | OS | 0 | u/severely reduced | No | 100 | 100 | Stable | 3 | 0.6 | 0.35±0.04 |
RP 5 | F | 36 | OD | 0.1 | u/u | No | 97 | 99 | Stable | 4 | 0.54 | 0.17±0.01 |
RP 6 | M | 38 | OD | 0 | u/severely reduced | No | 98 | 100 | Stable | 4 | 0.77 | 0.17±0.04 |
RP 7 | F | 43 | OD | 0.1 | u/u | No | 95 | 100 | Stable | 4 | 0.6 | 0.22±0.01 |
RP 8 | F | 31 | OD | 0.1 | u/u | No | 94 | 95 | Stable | 4 | 0.79 | 0.27±0.01 |
Fixation was classified as stable when 75% of fixations were located within a 2° circle, as relatively unstable when 75% of fixations were located within a 4° circle and as unstable when less than 75% of fixations were located within a 4° circle.
ERG, electroretinogram; F, female; fMRI, functional MRI; logMAR, logarithm of the minimum angle of resolution; M, male; MAE, mean average error; MP, microperimetry; n, normal; OD, right eye; OS, left eye; pRF, population-receptive field; RP, retinitis pigmentosa; STGD, Stargardt disease; VA, visual acuity; u, undetectable.