In this series, ten patients with systemic sarcoidosis presented with retinal changes as the initial manifestation of the disease. The diagnosis was suspected on the basis of the retinal findings, and subsequently substantiated by medical evaluation. Anterior uveitis, the best-known finding in ocular sarcoidosis, was overshadowed by the retinal changes. The retinal findings in this condition are characteristic and should alert the ophthalmologist to evaluate the patient for systemic sarcoidosis.